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  •   Ιδρυματικό Αποθετήριο Πανεπιστημίου Θεσσαλίας
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  •   Ιδρυματικό Αποθετήριο Πανεπιστημίου Θεσσαλίας
  • Επιστημονικές Δημοσιεύσεις Μελών ΠΘ (ΕΔΠΘ)
  • Δημοσιεύσεις σε περιοδικά, συνέδρια, κεφάλαια βιβλίων κλπ.
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Ιδρυματικό Αποθετήριο Πανεπιστημίου Θεσσαλίας
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Interstitial lung disease in anti-synthetase syndrome

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Συγγραφέας
Kourkouni E., Mitsogiannis G., Simopoulou T., Liaskos C., Katsiari C.G., Daniil Z., Gourgoulianis K., Bogdanos D.P., Sakkas L.I.
Ημερομηνία
2019
Γλώσσα
en
DOI
10.31138/mjr.30.3.186
Λέξη-κλειδί
antibody
antinuclear antibody
bronchodilating agent
C reactive protein
clarithromycin
cotrimoxazole
creatine kinase
Jo 1 antibody
methylprednisolone
moxifloxacin
oseltamivir
oxygen
piperacillin plus tazobactam
prednisolone
rituximab
Ro52 antibody
unclassified drug
adult
allergic pneumonitis
antisynthetase syndrome
arterial oxygen saturation
arthralgia
arthritis
Article
autoimmune disease
bronchiectasis
case report
Caucasian
clinical article
computer assisted tomography
differential diagnosis
drug dose reduction
drug megadose
dyspnea
fatigue
female
fever
follow up
forced expiratory volume
forced vital capacity
human
hypoxia
interstitial lung disease
laboratory test
lung disease
lung function test
lung infiltrate
medical history
middle aged
myalgia
myositis
oxygen therapy
prescription
Raynaud phenomenon
respiratory tract infection
rheumatic disease
rheumatoid arthritis
sarcoidosis
Sjoegren syndrome
systemic lupus erythematosus
systemic sclerosis
tachypnea
thorax radiography
vasculitis
Greek Rheumatology Society and Professional Association of Rheumatologists
Εμφάνιση Μεταδεδομένων
Επιτομή
Anti-synthetase syndrome is an autoimmune disorder characterized by the presence of autoantibodies against aminoacyl transfer RNA (tRNA) synthetases, and myositis, interstitial lung disease (ILD), arthritis, fever and Raynaud's phenomenon (RP). We present a 54-year-old woman, who complained of fatigue, low-grade fever, myalgias, arthralgias, RP and dyspnoea on exertion. Chest CT scan revealed features of interstitial lung disease. Due to rapid deterioration of her lung function, she required oxygen support. The patient did not respond to empiric treatment with antibiotics. Autoantibody testing was remarkable for ANA positivity (1/160) and high-titre anti-Jo1 positivity. A diagnosis of anti-synthetase syndrome was made and the patient was placed on high-dose corticosteroids and rituximab with significant improvement. At 1-year follow up, she remains in good condition, without the need for oxygen supplementation. © Kourkouni E, Mitsogiannis G, Simopoulou T, Liaskos C, Katsiari CG, Daniil Z, Gourgoulianis K, Bogdanos DP, Sakkas LI.
URI
http://hdl.handle.net/11615/75328
Collections
  • Δημοσιεύσεις σε περιοδικά, συνέδρια, κεφάλαια βιβλίων κλπ. [19735]

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    SARS-CoV-2 pathophysiology and its clinical implications: An integrative overview of the pharmacotherapeutic management of COVID-19 

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    Common manifestations of COVID-19 are respiratory and can extend from mild symptoms to severe acute respiratory distress. The severity of the illness can also extend from mild disease to life-threatening acute respiratory ...
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