Ascites in a patient with episodic angio-oedema and eosinophilia: Thinking outside the box
dc.creator | Rigopoulou E.I., Ioannou M., Papadamou G., Dalekos G.N. | en |
dc.date.accessioned | 2023-01-31T09:51:31Z | |
dc.date.available | 2023-01-31T09:51:31Z | |
dc.date.issued | 2017 | |
dc.identifier | 10.1136/bcr-2017-219467 | |
dc.identifier.issn | 1757790X | |
dc.identifier.uri | http://hdl.handle.net/11615/78510 | |
dc.description.abstract | Episodic angio-oedema with eosinophilia (EAE) or Gleich's syndrome is a rare condition characterised by recurrent episodes of oedema and eosinophilia, accompanied by urticaria, fever and weight gain. The presence of ascites has not been reported so far. We report a 21-year-old Caucasian woman who presented with marked ocular oedema and ascites. Laboratory evaluation revealed marked eosinophilia. During the last 3 months, three episodes of facial and neck oedema were reported, which resolved spontaneously over a period of 3-5 days. The diagnosis of EAE was established after exclusion of secondary causes (infections, allergic reactions, collagen diseases, neoplasms) and clonal disorders associated with marked eosinophilia. Low-dose steroids resulted in eosinophil decrease and complete resolution of symptoms, including ascites. This case highlights that ascites can be a very rare manifestation of EAE particularly if other more frequent causes of ascites have been excluded and the clinical and laboratory findings are supportive of EAE. © BMJ Publishing Group Ltd . | en |
dc.language.iso | en | en |
dc.source | BMJ Case Reports | en |
dc.source.uri | https://www.scopus.com/inward/record.uri?eid=2-s2.0-85018750686&doi=10.1136%2fbcr-2017-219467&partnerID=40&md5=de228806dbca2af3ec52ebf43f331cb6 | |
dc.subject | complement component C1q | en |
dc.subject | complement component C1q esterase inhibitor | en |
dc.subject | complement component C1s inhibitor | en |
dc.subject | complement component C3 | en |
dc.subject | complement component C4 | en |
dc.subject | complement inhibitor | en |
dc.subject | corticosteroid | en |
dc.subject | prednisolone | en |
dc.subject | unclassified drug | en |
dc.subject | steroid | en |
dc.subject | abdominal distension | en |
dc.subject | abdominal pain | en |
dc.subject | abdominal ultrasound | en |
dc.subject | adult | en |
dc.subject | angioneurotic edema | en |
dc.subject | Article | en |
dc.subject | ascites | en |
dc.subject | asthma | en |
dc.subject | bone marrow biopsy | en |
dc.subject | case report | en |
dc.subject | differential diagnosis | en |
dc.subject | drug dose reduction | en |
dc.subject | echography | en |
dc.subject | eosinophil count | en |
dc.subject | eosinophilia | en |
dc.subject | eye edema | en |
dc.subject | face edema | en |
dc.subject | female | en |
dc.subject | genetic screening | en |
dc.subject | Gleich syndrome | en |
dc.subject | hospital readmission | en |
dc.subject | human | en |
dc.subject | human tissue | en |
dc.subject | laboratory test | en |
dc.subject | low drug dose | en |
dc.subject | neck swelling | en |
dc.subject | physical examination | en |
dc.subject | protein blood level | en |
dc.subject | weight gain | en |
dc.subject | young adult | en |
dc.subject | Angioedema | en |
dc.subject | ascites | en |
dc.subject | eosinophilia | en |
dc.subject | treatment outcome | en |
dc.subject | Angioedema | en |
dc.subject | Ascites | en |
dc.subject | Eosinophilia | en |
dc.subject | Female | en |
dc.subject | Humans | en |
dc.subject | Steroids | en |
dc.subject | Treatment Outcome | en |
dc.subject | Young Adult | en |
dc.subject | BMJ Publishing Group | en |
dc.title | Ascites in a patient with episodic angio-oedema and eosinophilia: Thinking outside the box | en |
dc.type | journalArticle | en |
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